Pauci-immune Crescentic Glomerulonephritis: Case Report

Wisam Mnkana¹, Nikita Wong², Eman EL-Sawalhy^1, , Ahmed Abdelrahim¹, Hussein Gaith¹, Zhang Ping³ and Rabih Bazzi⁴

¹Department of Internal Medicine, Beaumont Hospital, Dearborn, MI

²Wayne State University, School of Medicine, Detroit, MI

³Pathology Department, Oakland University William Beaumont School of Medicine

⁴Division of Nephrology, Internal Medicine Department, Beaumont Hospital, Dearborn, MI

Cite this paper

Wisam Mnkana, Nikita Wong, Eman EL-Sawalhy, Ahmed Abdelrahim, Hussein Gaith, Zhang Ping and Rabih Bazzi. Pauci-immune Crescentic Glomerulonephritis: Case Report. American Journal of Medical Case Reports. 2022; 10(3):45-47. doi: 10.12691/AJMCR-10-3-1

Abstract

Pauci-immune glomerulonephritis ( PIGN) is a potentially life-threatening condition that progresses rapidly to renal failure within days or weeks. Here we present a 62 -year-old African American female who was found to have acute kidney injury at the time of presentation. Further workup including renal biopsy showed anti-neutrophilic cytoplasmic antibodies (ANCA) associated pauci-immune crescentic glomerulonephritis. The patient was started on steroids and cyclophosphamide however, the patient’s kidney function continued to get worse and required hemodialysis. Unfortunately, our patient passed away after two months of diagnosis secondary to cardiac arrest.

Keywords

Pauci immune glomerulonephritis, crescentic glomerulonephritis, survival

Copyright

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