Systemic Lupus Erythematosus Revealing Splenic Marginal Zone Lymphoma. A Case Report

Bel Feki N^1, , Smiti Khanfir M¹, Said F¹, Hamzaoui A¹, Ben Salem T¹, Ben Ghorbel I¹, Lamloum M¹, Ben Romdhane N¹ and Houman MH¹

¹Internal Medicine Department. University hospital of La Rabta, Tunis. Tunisia

Cite this paper

Bel Feki N, Smiti Khanfir M, Said F, Hamzaoui A, Ben Salem T, Ben Ghorbel I, Lamloum M, Ben Romdhane N and Houman MH. Systemic Lupus Erythematosus Revealing Splenic Marginal Zone Lymphoma. A Case Report. American Journal of Medical Case Reports. 2015; 3(2):40-41. doi: 10.12691/AJMCR-3-2-6

Abstract

Autoimmune manifestations are common in splenic marginal zone lymphoma (SMZL) and are sometimes the presenting feature of the disease. We report Herein the case of a 72-year old woman presenting with systemic lupus erythematosus revealing SMZL. To our knowledge, there are only 3 case reports of SLE associated to SMZL. In case of authentic autoimmune disease with unusual clinical features Physician awareness is recommended, to rule out associated lymphoproliferative syndrome.

Keywords

systemic lupus erythematosus, splenic marginal zone lymphoma

Copyright

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