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American Journal of Medical Case Reports. 2016, 4(1), 8-11
DOI: 10.12691/AJMCR-4-1-3
Case Report

A Rare Presentation of Medullary Carcinoma Thyroid

Balakrishnan valliyot1, Saroshkumar KK1, Sarin SM1, Kadeeja beevi B1, Nirmal mathew alex1, and Tency joshu thomas1

1Department of Medicine, ACME Pariyaram, Kannur, India

Pub. Date: January 08, 2016
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Cite this paper

Balakrishnan valliyot, Saroshkumar KK, Sarin SM, Kadeeja beevi B, Nirmal mathew alex and Tency joshu thomas. A Rare Presentation of Medullary Carcinoma Thyroid. American Journal of Medical Case Reports. 2016; 4(1):8-11. doi: 10.12691/AJMCR-4-1-3

Abstract

Medullary Thyroid Carcinoma (MTC) is a rare thyroid tumor that arises from neural crest-derived Calcitonin producing Para follicular C cells and accounts for approximately 4 % of thyroid malignancies. This neuroendocrine tumor typically is an aggressive cancer, with secretion of several neuro-humoral mediators. We report a case of 49 year old male patient who presented with episodes of chest discomfort and abdominal pain associated with loud screaming of unknown etiology, on evaluation found to have Medullary Thyroid Carcinoma as its cause. MTC usually present as palpable firm to hard thyroid nodules or enlargement of regional lymph nodes. Since the systemic symptoms of MTC are nonspecific, it is challenging to diagnose MTC when patients first presents with systemic symptoms as in our patient. This case is reported to highlight the unusual presentation of this rare thyroid tumor and to emphasize the need for meticulous clinical examination and high index of suspicion to diagnose it.

Keywords

medullary carcinoma thyroid, thyroid malignancy, neurohormones

Copyright

Creative CommonsThis work is licensed under a Creative Commons Attribution 4.0 International License. To view a copy of this license, visit http://creativecommons.org/licenses/by/4.0/

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