A unique Presentation of Granulomatosis with Polyangiitis in a Patient of African-Caribbean Descent

Stefan Rodic^1, and Richard Dunbar-Yaffe²

¹Schulich School of Medicine, Western University, London, Canada

²Division of General Internal Medicine, University of Toronto, Toronto, Canada

Cite this paper

Stefan Rodic and Richard Dunbar-Yaffe. A unique Presentation of Granulomatosis with Polyangiitis in a Patient of African-Caribbean Descent. American Journal of Medical Case Reports. 2018; 6(1):12-14. doi: 10.12691/AJMCR-6-1-4

Abstract

Herein, we present a case of limited granulomatosis with polyangiitis (GPA) with ocular/aural involvement and sparing of the visceral organs. This atypical constellation of symptoms was initially thought to have an infectious cause prior to repeat imaging and testing of immunological markers. The patient was of African-Caribbean descent, a population where the incidence of granulomatosis with polyangiitis is exceedingly uncommon. This case highlights a unique variant of GPA and emphasizes the importance of early clinical detection and treatment to prevent associated morbidity and mortality.

Keywords

granulomatosis, polyangiitis, vasculitis, GPA, ocular, aural, ANCA

Copyright

This work is licensed under a Creative Commons Attribution 4.0 International License. To view a copy of this license, visit http://creativecommons.org/licenses/by/4.0/

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