American Journal of Medical Case Reports. 2018, 6(2), 21-23
DOI: 10.12691/AJMCR-6-2-2
Clival Chordoma in Children a Rare Condition: Case Report
Ali Al Mashni1, Neeraj Salhotra1, , Mohammad Hadad1, Mohammad Hashim1, Tariq Al Saidi1 and Samit Biniwal1
1Neurosurgeon Khoula Hospital Muscat Oman
Pub. Date: March 07, 2018
Cite this paper
Ali Al Mashni, Neeraj Salhotra, Mohammad Hadad, Mohammad Hashim, Tariq Al Saidi and Samit Biniwal. Clival Chordoma in Children a Rare Condition: Case Report.
American Journal of Medical Case Reports. 2018; 6(2):21-23. doi: 10.12691/AJMCR-6-2-2
Abstract
A three year child had presented to our OPD with complaints of nasal obstruction, change of voice and difficulty in ingestion. Patient was investigated and was seen having a mass in the nasopharynx. Further investigations revealed on CT and MRI brain a large tumour destroying the clival region with nasopharyngeal and intracranial extension with pressure effect on brain stem and lower cranial nerves. Patient underwent two stage surgery retromastoid craniectomy with excision of intracranial part and later a tracheostomy and transoral excision of the nasopharyngeal extension and part anterior to brain stem. Patient made a remarkable recovery and was discharged home after tracheostomy removal with advice to follow with pediatric oncology for chemotherapy as HPE revealed it to be clival chordoma a rare entity in children.
Keywords
clival chordoma in children
Copyright
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References
[1] | Diagnosis of clival chordoma by fine needle aspiration of an oropharyngeal mass. A case report Hazarika D, Kumar RV, Muniyappa GD, Mukherjee G, Rao CR, Narasimhamurthy NK, Shenoy AM, Nanjundappa. Acta Cytol. 1995 May-Jun; 39(3): 507-10. |
|
[2] | Cranial chordoma in the first decade. Yadav YR, Kak VK, Khosla VK, Khandelwal N, Radotra BD.Clin Neurol Neurosurg. 1992; 94(3): 241-6. |
|
[3] | Paediatric Chordomas. Beccaria K, Sainte-Rose C, Zerah M, Puget S Orphanet J Rare Dis. 2015 Sep 22; 10: 116. |
|
[4] | Intradural prepontine chordoma in an 11-year-old boy. A case report.Vinke RS, Lamers EC, Kusters B, van Lindert EJ. Childs Nerv Syst. 2016 Jan; 32(1): 169-73. |
|
[5] | Juvenile intradural chordoma: case report.Chang SW, Gore PA, Nakaji P, Rekate HL. Neurosurgery. 2008 Feb; 62(2): E525-6. |
|
[6] | Intradural chordoma of the tentorium cerebelli. Case report. Warnick RE, Raisanen J, Kaczmar T Jr, Davis RL, Prados MD J Neurosurg. 1991 Mar; 74(3): 508-11. |
|