Juvenile Dermatomyositis Associated to Familial Mediterranean Fever

Salem Bouomrani^{1, 2,} , Rim Mesfar^{1, 2}, Moez BenAyed^{2, 3}, Mouna Guermazi^{1, 2}, Hassène Baïli¹ and Souad Yahyaoui¹

¹Department of Internal Medicine, Military Hospital of Gabes, Gabes 6000, Tunisia

²Sfax Faculty of Medicine, University of Sfax, Sfax 3029, Tunisia

³Department of Orthopedics, Regional Hospital of Gabes, Gabes 6000, Tunisia

Cite this paper

Salem Bouomrani, Rim Mesfar, Moez BenAyed, Mouna Guermazi, Hassène Baïli and Souad Yahyaoui. Juvenile Dermatomyositis Associated to Familial Mediterranean Fever. American Journal of Medical Case Reports. 2019; 7(8):170-172. doi: 10.12691/AJMCR-7-8-5

Abstract

Familial Mediterranean Fever (FMF) is a rare hereditary auto-inflammatory disease that can be exceptionally associated with many other dys-immune disorders; the most reported associations were with systemic vasculitis, spondyloarthropathies, inflammatory bowel diseases, systemic lupus erythematous, multiple sclerosis, and juvenile chronic arthritis. The association of FMF with primary inflammatory myopathy remains exceptional and unusual; it has only been noted once before with adult polymyositis. We report an original observation of FMF associated with juvenile dermatomyositis in an eight-year-old boy, which, to our knowledge, has not been reported previously.

Keywords

familial mediterranean fever, juvenile dermatomyositis, dermatomyositis

Copyright

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