Fatal Case of Dysphagia Induced by Neurofibromatosis Type II

Ken-ichi Muramatsu¹, Hiroki Nagasawa¹, Soichiro Ota¹, Kei Jitsuiki¹, Hiromichi Ohsaka¹ and Youichi Yanagawa^1,

¹Department of Acute Critical Care Medicine, Shizuoka Hospital, Juntendo University, Japan

Cite this paper

Ken-ichi Muramatsu, Hiroki Nagasawa, Soichiro Ota, Kei Jitsuiki, Hiromichi Ohsaka and Youichi Yanagawa. Fatal Case of Dysphagia Induced by Neurofibromatosis Type II. American Journal of Medical Case Reports. 2021; 9(10):507-508. doi: 10.12691/AJMCR-9-10-7

Abstract

A 17-year-old boy was found in an unconscious state. He had had neurofibromatosis type 2 (NF2) since 9 years old. His history included multiple operations for NF2 at the left jugular vein foramen, thoracic spinal cord, and cervical spinal cord at 9 and 10 years old. However, remaining bilateral acoustic tumors resulted in the onset of aspirated pneumonia within a few months. He was found unconscious in his dormitory. When emergency medical technicians checked him, he was in cardiac arrest. Saburra was identified in his mouth. He did not achieve return of spontaneous circulation with advanced cardiac life support. Autopsy imaging revealed residual bilateral acoustic tumors compressing the brain stem. NF2 is a serious disease that can rapidly become life-threatening. We hope new treatments that will improve the survival of NF2 patients will be developed soon.

Keywords

neurofibromatosis, fatality, dysphagia

Copyright

This work is licensed under a Creative Commons Attribution 4.0 International License. To view a copy of this license, visit http://creativecommons.org/licenses/by/4.0/

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